Myelopathy secondary to copper deficiency as a complication of treatment of Wilson’s disease
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منابع مشابه
Wilson’s Disease: Nutrition Support
Wilson’s disease (WD) or hepato-lenticular degeneration is a rare autosomal-recessive disorder. A prevalence rate of 30 cases per million and a birth incidence rate of one per 30,000 to 40,000 are often quoted. In 40 to 50% of individuals with WD, hepatic dysfunction is the initial clinical manifestation. With the exception of liver transplantation, treatment of WD is only palliative and intend...
متن کاملMyelopathy secondary to copper deficiency as a complication of treatment of Wilson's disease.
Wilson's Disease (WD) is an autosomal recessive disorder of copper metabolism resulting in a pathological accumulation of this metal, initially in the liver and later in other organs, mainly brain. Treatment with copper chelating agents and zinc salts results in a depletion of copper deposits and prevents or reverses the clinical manifestations. Copper deficiency may cause haematological and ne...
متن کاملMyelopathy due to copper deficiency following gastrointestinal surgery.
BACKGROUND Ataxic myelopathy due to copper deficiency has been described in ruminant animals and is called swayback. Neurological manifestations due to inherited copper deficiency secondary to the failure of intestinal copper absorption is well recognized as Menkes disease. The neurological consequences of acquired copper deficiency in humans are not well described. OBJECTIVE To report 2 case...
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Recurrent miscarriage is a less recognized feature of Wilson’s disease and adequate treatment can alter the outcome of pregnancies favourably. Wilson’s disease is a recessively inherited disorder of copper metabolism due to mutations in the ATP7B gene, which encodes for a coppertransporting P-type ATPase. Recurrent miscarriage is a complication of untreated Wilson’s disease. It has been reporte...
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تاریخ انتشار 2013